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WHO Classification of Tumours
Lymphangioma, NOS
Kidney


Definition

Lymphangioma is a benign cavernous/cystic vascular lesion composed of dilated lymphatic channels. They constitute common paediatric lesions, which most often present at birth or during first years of life. Cavernous/cystic lymphangioma of head and neck are most common. Some lymphangiomas occur in the setting of Turner syndrome and other malformative syndromes
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Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



. Painless swelling is the usual clinical manifestation.

Lymphangioma of the kidney is rare and usually presents as a peripelvic or renal sinus mass. Renal lymphangiomas are encapsulated, diffusely cystic lesions ranging from small well-delineated tumours to large lesions that may replace the entire renal parenchyma. The cysts communicate, contain clear fluid, and are composed of fibrous septae lined by flattened endothelium

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Eble JE, Sauter G, Epstein JI, Sesterhenn IA (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Urinary System and Male Genital Organs.
3rd Edition
IARC Press: Lyon 2004



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