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WHO Classification of Tumours
Haemangiopericytoma
Kidney


Definition

Haemangiopericytoma (HPC) is a mesenchymal tumour histologically characterized by dilated vascular spaces, often with a staghorn or bifed shape. Individual tumour cells are surrounded by a reticulin network and are positive for CD34 and CD99. Haemangiopericytomas closely resemble cellular areas of solitary fibrous tumour (SFT) and and are closely related to, if not synonymous with, SFT. Lesions formerly known as infantile HPC fall within the spectrum of infantile myofibromatosis
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Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



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Primary renal haemangiopericytomas are extremely rare. Most of them arise in the renal sinus and in perirenal tissue. Tumours are large, firm, and histologically composed of fusiform pericytes separated by capillaries with the typical staghorn configuration

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Eble JE, Sauter G, Epstein JI, Sesterhenn IA (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Urinary System and Male Genital Organs.
3rd Edition
IARC Press: Lyon 2004



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