logo logo
Search: Organ site Search: Tumor / Syndrome
WHO Classification of Tumours
Desmoplastic small round cell tumor
Testis/Male genital organs


An aggressive malignant neoplasm of uncertain lineage. It is characterized by the presence of small round cells in a desmoplastic stroma. It usually affects children and young adults. The most common site of involvement is the abdomen. Patients usually present with abdominal distention, pain, ascites, and a palpable abdominal mass. The prognosis is usually poor.