Rhabdomyosarcoma is a rare aggressive mesenchymal tumour composed of cells with varying degrees of skeletal muscle differentiation.
Primary rhabdomyosarcoma in pure form is very uncommon in the breast. Most primary tumours are either of the alveolar
or of the pleomorphic
subtype; typically, the alveolar type arises in adolescents
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, whereas the pleomorphic type is observed in women >40 years of age
Breast malignancy in children.
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. The majority of mammary rhabdomyosarcoma represent metastases from a soft tissue rhabdomyosarcoma occurring in children and young adults. These metastases are predominantly of the alveolar subtype
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