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WHO Classification of Tumours
Alveolar soft part sarcoma
Connective, subcutaneous and other soft tissues


A rare malignant neoplasm histologically characterized by the presence of large epithelioid cells with abundant cytoplasm forming nests and pseudoalveolar structures. Groups of the epithelioid cells are separated by thin-walled sinusoidal spaces. In adults the most common sites of involvement are the extremities, in infants and children the head and neck region. It usually presents as a slowly growing mass and it frequently metastasizes to other anatomic sites. The most common sites of metastasis are the lungs, bone, and brain
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Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002