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WHO Classification of Tumours
Malignant peripheral nerve sheath tumor
Nasal cavity and Sinuses


Definition

An uncommon, highly aggressive malignant tumor, arising from the peripheral nerves and affecting mostly adults in their third to sixth decades of life. It usually occurs in medium-sized and large nerves of the buttock, thigh, upper arm, or the paraspinal region.
MPNST may be associated with neurofibromatosis type 1 (NF1).