logo logo
Search: Organ site Search: Tumor / Syndrome
or
WHO Classification of Tumours
Rhabdomyosarcoma, NOS
Esophagus


Definition

A rare aggressive malignant mesenchymal neoplasm arising from skeletal muscle. It usually occurs in children and young adults. Only a small percentage of tumors arise in the skeletal muscle of the extremities. The majority arise in other anatomical sites.

In the oesophagus, only a small number of well-documented rhabdomyosarcomas (of embryonal type) have been reported . These tumours have occurred in the distal oesophagus in older adults

Click to access Pubmed
Vartio T, Nickels J, Höckerstedt K, Scheinin TM (1980)
Rhabdomyosarcoma of the oesophagus. Light and electron microscopic study of a rare tumor.
Virchows Arch A Pathol Anat Histol 386: 357-61



. Immunohistochemical demonstration of desmin and nuclear expression of myogenic regulatory proteins (MyoD1 or myogenin) is required for diagnosis.